Testicular mass: a rare presentation of Richter's syndrome

Abstract Background Richter’s syndrome is the transformation of indolent lymphoma into an aggressive form, most commonly diffuse large B cell lymphoma. Most patients are known to have chronic lymphocytic leukemia. arises in lymph nodes or bone marrow and rarely presents with extra nodal involvement. Case presentation Our patient presented at extremely uncommon site, i.e., testis. This fourth case reported literature. Moreover, our represents longest follow-up so far recurrence-free survival more than 2 years now. Conclusion Testicular mass a history leukemia should raise clinical suspicion accordingly be thoroughly investigated treated. Treatment needs multidisciplinary team approach: urologist, pathologist hematologist.